Asian Journal of Case Reports in Surgery

Robotic-Assisted Bilateral Cortical Sparing Adrenalectomy in a Case of Bilateral Familial Pheochromocytoma: A Case Report and Review of Literature

Saloni Chheda *

Fortis Hospital Mulund, Mulund-Goregoan Link Road, Nahur West, Industrial Area, Mumbai-400078, Maharashtra, India.

Apoorva Pawar

Fortis Hospital Mulund, Mulund-Goregoan Link Road, Nahur West, Industrial Area, Mumbai-400078, Maharashtra, India.

Saurabh Ramesh Patil

Fortis Hospital Mulund, Mulund-Goregoan Link Road, Nahur West, Industrial Area, Mumbai-400078, Maharashtra, India.

Arun Behl

Fortis Hospital Mulund, Mulund-Goregoan Link Road, Nahur West, Industrial Area, Mumbai-400078, Maharashtra, India.

P. S. Lamba

Fortis Hospital Mulund, Mulund-Goregoan Link Road, Nahur West, Industrial Area, Mumbai-400078, Maharashtra, India.

Bipin Daxini

Fortis Hospital Mulund, Mulund-Goregoan Link Road, Nahur West, Industrial Area, Mumbai-400078, Maharashtra, India.

*Author to whom correspondence should be addressed.

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Abstract

Although bilateral pheochromocytomas are frequently encountered in familial cases, a cortical-sparing approach outweighs the need for total adrenalectomy and its continuing repercussions of lifelong steroid dependency. Hereby highlighting a case of boy with bilateral pheochromocytomas managed with bilateral cortical sparing adrenalectomy. Multi-disciplinary approach and a minimal invasive technique aided the management and delayed the need for life-long steroid supplementation.

Keywords: Familial pheochromocytoma, bilateral pheochromocytoma, bilateral adrenalectomy, cortical sparing adrenalectomy

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