Asian Journal of Case Reports in Surgery

Congenital Triple Atresia Involving Esophageal Atresia, Duodenal Atresia and Imperforated Anus: An Uncommon Presentation

Nitin Jain

Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi – 110002, India.

Simmi K. Ratan *

Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi – 110002, India.

*Author to whom correspondence should be addressed.

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Abstract

Triple atresia a rare entity comprises of esophageal atresia(EA), duodenal atresia(DA) and anorectal malformation(ARM). The association of esophageal atresia with tracho-esophageal fistula and anorectal malformation is relatively common while association with duodenal atresia is uncommon with the reported incidence is less than 1% to 2%. Here we report a case of triple atresia involving the esophagus, duodenum and anorectum, where all three entities were diagnosed at the time of admission and surgical correction of esophageal atresia, duodenal atresia along with sigmoid colostomy for high ano-rectal malformation, was carried out as the first stage. A high index of suspicion for the detection of coexisting gastrointestinal anomalies is mandatory in the management EA patients, to avoid undue morbidity and mortality.

Keywords: Anorectal malformation (ARM), duodenal atresia, esophageal atresia, triple atresia, tracheoesophageal fistula (TEF)

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